- See:
vascular malformations of the upper extremity
- Clinical Presentation:
- usually begins incidiously
- vague weakness, wt loss, diffuse stiffness, aching, burning polyarticular arthritis;
- diffus edema of hands;
- skin and GI manifestations are common;
-
hand:
- skin is taut, thickened, or edematous & is bound tightly to subQ tissues;
- normal skin folds at the knuckles disappear;
- chronic recurrent painful ulcerations appear at ends of digits;
-
Raynaud's phenomenon is common;
- hyperhidrosis, finger stiffness of fingers;
- ulcerations fingertip amputation;
- Radiographs:
- diffuse subQ
calcifications (calcinosis circumscripta) are seen;
- Labs: sed rate is elevated;
- Treatment:
- sympathectomy:
